Just found interesting paper about Williams syndrome and the fusiform face area

It appears that having a fusiform face area (FFA) that is twice the normal size does not give people with Williams syndrome (WS) super powers of face recognition or expression recognition, but I’m not sure we can be completely sure that people with Williams do not have any special gift in reading faces, as other researchers have found fault with the test that was used in this study to measure face recognition ability. Williams syndrome is a genetic syndrome that is associated with  intellectual deficits, “heightened emotionality”, “hypersociability” and a special love of music. Dr Oliver Sacks wrote an interesting chapter about Williams syndrome in his book Musicophilia. I do not have Williams syndrome, and this syndrome does not run in my family. One thing that I do believe that I and some family members share in common with people who have Williams syndrome is our great love of music, despite a lack of musical education or training.

“The atypically large FFA volume that we found in WS was positively correlated with apparently normal performance levels on a standardized face-identity recognition task (Benton test) in the same participants. This finding is analogous to electrophysiological reports of atypically large N200 in WS, which is correlated with performance on the Benton test (Mills et al., 2000). However, in our experiments, the correlation between rFFA size and Benton scores reached statistical significance only after excluding two WS participants with the noisiest BOLD signals. The similarity in the mean performance across TD and WS in the Benton test may be due to insufficient sensitivity of the Benton test in detecting subtle variations in face-recognition proficiency (Duchaine and Nakayama, 2004).”

Has anyone ever done a study in which people who have Williams syndrome have been given the Cambridge Face Memory Test (CFMT)? I’d love to read that.

Golijeh Golarai, Sungjin Hong, Brian W. Haas, Albert M. Galaburda, Debra L. Mills, Ursula Bellugi, Kalanit Grill-Spector & Allan L. Reiss The Fusiform Face Area is Enlarged in Williams Syndrome. Journal of Neuroscience. 12 May 2010, 30(19): 6700-6712; doi: 10.1523/​JNEUROSCI.4268-09.2010
http://www.jneurosci.org/content/30/19/6700.full

Duchaine, Bradley & Nakayama, Ken Developmental prosopagnosia and the Benton Facial Recognition Test. Neurology. April 13, 2004 vol. 62 no. 7 1219-1220. doi: 10.1212/01.WNL.0000118297.03161.B3 http://www.neurology.org/content/62/7/1219.abstract

“The Benton Facial Recognition Test is used for clinical and research purposes, but evidence suggests that it is possible to pass the test with impaired face discrimination abilities.”

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